Intrathoracic manifestation in Rosai Dorfman Disease (RDD): A case report with review of the literature

  • Sulav Sapkota
  • Mona Priyadarshini
  • Srinivasa BJ
  • Bhanu Prakash Lalkota
  • Shivakumar Swamy
  • Radheshyam Naik

Abstract

Rosai-Dorfman disease, previously known as sinus histiocytosis with massive lymphadenopathy (SHML) is one of the rare benign idiopathic proliferative diseases of phagocytic histiocytes. Majority of the patients present with painless massive cervical lymphadenopathy but intrathoracic involvement is rarely reported. Here, we report the case of a 57-year-old male with a history of chest pain, shortness of breath and generalized weakness of two-month duration. The diagnosis was formed by core biopsy of the axillary lymph node with typical emperipolesis and Immunohistochemistry markers

Keywords: Emperipolesis, Immunohistochemistry,. Rosai Dorfman disease.
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How to Cite
Sapkota, S., Priyadarshini, M., BJ, S., Lalkota, B., Swamy, S., & Naik, R. (2019). Intrathoracic manifestation in Rosai Dorfman Disease (RDD): A case report with review of the literature. Indian Journal of Case Reports, 5(3). Retrieved from https://atharvapub.net/IJCR/article/view/1512
Section
Case Report