Dyke-Davidoff-Masson syndrome: A case report

  • Piyush Chaudhary
  • Archana Agrawal
  • Ankur Malhotra
  • Akhil Bangari

Abstract

A 7 years girl presented with seizures, intellectual disability, right sided spastic cerebral palsy, and strabismus of right eye. Magnetic
resonance imaging (MRI) brain was suggestive of severe volume loss of brain parenchyma with dilatation of ipsilateral lateral
ventricle, and other MRI features diagnostic of infantile type Dyke-Davidoff-Masson syndrome also termed as cerebral hemiatrophy.
Seizures can be refractory to medical treatment and surgical treatment may become necessary. Greater awareness about the disease
is required to diagnose the condition timely and refer to neurosurgery in the case of refractory seizures as hemispherectomy is the
treatment of choice with high success rate.

Keywords: Calvarium thickening, Cerebral hemi atrophy, Dyke-Davidoff-Masson syndrome, Infantile, Intellectual disability, Refractory seizures
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How to Cite
Chaudhary, P., Agrawal, A., Malhotra, A., & Bangari, A. (2017). Dyke-Davidoff-Masson syndrome: A case report. Indian Journal of Child Health, 4(4), 626-628. Retrieved from https://atharvapub.net/IJCH/article/view/381
Section
Case Reports